Branch retinal artery occlusion in Susac's syndrome

Susac's syndrome is a rare disease attribuited to a microangiopathy involving the arterioles of the cochlea, retina and brain. Encefalopathy, hearing loss, and visual deficits are the hallmarks of the disease. Visual loss is due to multiple, recurrent branch arterial retinal occlusions. We report a case of a 20-year-old women with Susac syndrome presented with peripheral vestibular syndrome, hearing loss, ataxia, vertigo, and vision loss due occlusion of the retinal branch artery.

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Bibliographic Details
Main Authors: Aragão,Ricardo Evangelista Marrocos de, Gomes,Lorena Maria Araújo, Barreira,Ieda Maria Alexandre, Oliveira Neto,Francisco Holanda, Bastos,Ariane Sá Vieira
Format: Digital revista
Language:English
Published: Sociedade Brasileira de Oftalmologia 2015
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0034-72802015000100040
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Description
Summary:Susac's syndrome is a rare disease attribuited to a microangiopathy involving the arterioles of the cochlea, retina and brain. Encefalopathy, hearing loss, and visual deficits are the hallmarks of the disease. Visual loss is due to multiple, recurrent branch arterial retinal occlusions. We report a case of a 20-year-old women with Susac syndrome presented with peripheral vestibular syndrome, hearing loss, ataxia, vertigo, and vision loss due occlusion of the retinal branch artery.