Hemipelvectomy with laparoscopic abdominoperineal excision for epithelioid sarcoma treatment

Abstract The epithelioid sarcoma (ES) is an unusual variant of the sarcoma, not reaching 1% of all soft tissue sarcomas. Initially reported in 1970, it has a more aggressive variant, which was classified as the “proximal-type” in 1997. These are aggressive tumors with high rates of distant metastasis and local relapses. Isolated radio and chemotherapy responses are poor and free-margin surgical resection is the treatment of choice.This is the case report of a 25-year-old male patient diagnosed with “proximal-type” ES in the perineal region. He underwent surgical resection in another institution and was later admitted to our institution with local recurrence with rectal and left thigh muscle invasion. Neoadjuvant radio-chemotherapy was performed, followed by laparoscopic abdominoperineal rectal resection and partial left hemipelvectomy associated with left lower-limb amputation. The patient had no postoperative complications and is currently undergoing outpatient follow-up. The anatomopathological analysis showed tumor-free margins.The “proximal-type” ES is a rare soft-tissue sarcoma subtype. High local recurrence, as well as the metastasis rates, makes its treatment a challenging task.

Bibliographic Details

Main Authors:	Santana,Daniel Paulino, Meyer,Matheus Matta Machado Mafra Duque Estrada, Santos,Edmilson Celso, Andrade,Camila Gomes de Souza, Vilela Neto,Paulo, Matoso,Aline Alves, Santos,Bruna Sílvia Torres, Silva,Bruno José Guedes, Ferreira,Danielle Bossi Grassi, Horta,Larissa Vasconcelos, Reis,Marcos Campos Wanderley
Format:	Digital revista
Language:	English
Published:	Sociedade Brasileira de Coloproctologia 2017
Online Access:	http://old.scielo.br/scielo.php?script=sci_arttext&pid=S2237-93632017000300247
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