Orthodontic-surgical treatment of a patient with Marfan Syndrome and Obstructive Sleep Apnea Syndrome: a case report with a 9-year follow-up

ABSTRACT Marfan’s (MFS) syndrome is characterized by a defect in the connective tissue, which affects multiple organic systems. Therefore, the management of these patients requires a multidisciplinary approach. This case reports the orthodontic-surgical treatment of a patient who presented both Marfan’s and obstructive sleep apnea syndrome. Patient had malocclusion, TMJ clicking, vertical maxillary excess, mandibular retrognathia, severe esthetic compromise, signs and symptoms of obstructive sleep apnea syndrome, as well as alterationsin joints, cardiovascular and respiratory systems. He was treated with bimaxillary surgery aimed to enhance esthetics, occlusion and address the obstructive sleep apnea syndrome. The clinical results show that a desirable functional occlusion was achieved and both patient’s facial esthetics and quality of life were significantly improved. After a 9-year follow-up period, these pleasing features were maintained. The diagnosis and management of Marfan’s patients is challenging and require multidisciplinary follow-up.

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Bibliographic Details
Main Authors: RODRIGUES,Willian Caetano, GABRIELLI,Mário Francisco Real, OLIVEIRA,Marina Reis, PIVETA,Ana Cláudia Gabrielli, GABRIELLI,Marisa Aparecida Cabrini
Format: Digital revista
Language:English
Published: Faculdade São Leopoldo Mandic 2019
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372019000100816
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