Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases

ABSTRACT Creutzfeldt-Jacob disease (CJD) is a rare condition caused by a pathogenic prion protein that evolves with rapidly progressive dementia and death. The clinical presentation may sometimes be misleading. Magnetic Resonance Imaging (MRI) aids diagnosis with patterns that can guide or confirm clinical hypotheses. Two cases of rapidly progressive dementia with ataxia, myoclonus and restricted diffusion on MRI in cortical/basal ganglia are presented to draw attention to CJD.

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Bibliographic Details
Main Authors: Valente,Alan Peres, Pinho,Paula da Cunha, Lucato,Leandro Tavares
Format: Digital revista
Language:English
Published: Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento 2015
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424
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