Autopsy findings of a child with left atrial isomerism associated with pulmonary agenesis

Autopsy findings of a child with left atrial isomerism associated with pulmonary agenesis

ABSTRACT Isomerism is a rare laterality defect. Our aim was to describe the autopsy findings of a child with left atrial isomerism (LAI) and pulmonary agenesis (PA), an association still not described in the literature. Fetal ultrasound revealed right renal agenesis, single umbilical artery and polyhydramnios. Echocardiography revealed a complex heart defect with LAI. The child died minutes after birth. Autopsy confirmed the prenatal findings and revealed the presence of unilateral PA, complex vascular abnormalities and polysplenia. Despite its rarity, health professionals should be aware for the possibility of such an association.

Saved in:
Bibliographic Details
Main Authors: Pereira,Camilla M. V., Cruz,Larissa V., Girotto,Marina C., Cunha,André C., Telles,Jorge Alberto B., Diniz,Bruna L., Rosa,Rosana C. M., Zen,Paulo Ricardo G., Rosa,Rafael Fabiano M.
Format: Digital revista
Language:English
Published: Sociedade Brasileira de Patologia Clínica 2018
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1676-24442018000200109
Tags: Add Tag
No Tags, Be the first to tag this record!

Internet

http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1676-24442018000200109

Similar Items