Multicentric pheochromocytoma and involvement of the inferior vena cava

CONTEXT: Extension of pheochromocytomas to the inferior vena cava is rare. Multicentric tumors are rare as well, being present in up to 10% of cases. Surgery is the treatment of choice because of the long-term survival free of disease. DESIGN: Case report. CASE REPORT: We report on a case of right adrenal pheochromocytoma with extension to the supra-diaphragmatic vena cava, which underwent surgical excision through thoracophrenic laparotomy without the need for cardiopulmonary bypass. In a 6-year follow-up, another pheochromocytoma was found in the infra-renal Zuckerkandl's organ. Complete surgical excision of the tumor was performed by a median laparotomy and complete retroperitoneal dissection. In both cases, the total removal of the pheochromocytoma has been guaranteed by having margins free of tumor and a normal post-operative level of catecholamines. The pathological study revealed a malignant pheochromocytoma with margins free of neoplasia in both specimens.

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Bibliographic Details
Main Authors: Lucon,Antonio Marmo, Falci Júnior,Renato, Praxedes,José Nery, Machado,Marcel Cerqueira Cesar, Saldanha,Luis Balthazar, Machado,Marcelo Marcondes, Arap,Sami
Format: Digital revista
Language:English
Published: Associação Paulista de Medicina - APM 2001
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31802001000200010
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