Case for diagnosis. Lichen myxedematosus

Abstract Scleromyxedema or lichen myxedematosus is a rare papular mucinosis of chronic and progressive course and unknown etiology. It is commonly associated with monoclonal gammopathy and may show extracutaneous manifestations, affecting the heart, lung, kidney, and nerves. The diagnosis is based on four criteria: generalized papular and sclerodermoid lesions; mucin deposition, fibroblast proliferation, and fibrosis in the histopathology; monoclonal gammopathy; and no thyroid disorders. This article reports the case of a scleromyxedema patient with a recent history of acute myocardial infarction and monoclonal gammopathy.

Saved in:
Bibliographic Details
Main Authors: Rebellato,Priscila Regina Orso, Carbonar,Mauren Beatriz Frazon, Tabuti,Nicole Iasmin Magario, Rastelli,Graziela Junges Crescente
Format: Digital revista
Language:English
Published: Sociedade Brasileira de Dermatologia 2016
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016000600842
Tags: Add Tag
No Tags, Be the first to tag this record!