Progressive symmetrical erythrokeratodermia - Case report*

Progressive symmetrical erythrokeratodermia is a rare autosomal dominant genodermatosis with variable penetrance described by Darier in 1911. It is characterized by erythematous and keratotic plaques, sharply defined and symmetrically distributed along the extremities, buttocks and, more rarely, on the face. We report a case of a 55-year-old patient with lesions on the dorsum of the hands, interphalangeal pads, wrists, groin and back feet. This case demonstrates a rare and late diagnosis, clinical profusion and presence of familiar involvement.

Saved in:
Bibliographic Details
Main Authors: Guaraldi,Bianca de Mello, Jaime,Thaís Jerez, Guaraldi,Rafael de Mello, Melo,Daniel Fernandes, Nogueira,Osvania Maris, Rodrigues,Nilton
Format: Digital revista
Language:English
Published: Sociedade Brasileira de Dermatologia 2013
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000100109
Tags: Add Tag
No Tags, Be the first to tag this record!