Primary Ewing sarcoma/primitive neuroectodermal tumor of the lung

ABSTRACT We present the autopsy findings and differential diagnosis in a 42year old male who presented with fever and rapidly progressive respiratory symptoms like breathlessness, nonproductive cough and right sided chest pain. Initial imaging workup done at our hospital revealed a large unilateral tumor with tracheal shift. While being evaluated patient developed facial puffiness, tachypnea suggestive of superior vena cava obstruction. Antemortem biopsy of lung mass was attempted twice and that suggested malignant lesion. Unfortunately, the individual had a rapid downhill course following admission. Post mortem examination was conducted that on opening the thoracic cavity revealed total replacement of right lung tissue by a necrotic growth which was deeply adherent to the rib cage. The contralateral lung as well as all other visceral organs were unremarkable grossly. Histopathology confirmed primary Ewing sarcoma of the lung. We hereby, report a rare case of primary lung Ewing sarcoma diagnosed at autopsy.

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Main Authors: Gupta,Devika, Chatterjee,Tathagata, Tewari,Rohit, Trehan,Arti, Ahuja,Anuradha
Format: Digital revista
Language:English
Published: Hospital Universitário da Universidade de São Paulo 2020
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S2236-19602020000300401
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spelling oai:scielo:S2236-196020200003004012020-11-09Primary Ewing sarcoma/primitive neuroectodermal tumor of the lungGupta,DevikaChatterjee,TathagataTewari,RohitTrehan,ArtiAhuja,Anuradha Ewing sarcoma extraosseous Lung ABSTRACT We present the autopsy findings and differential diagnosis in a 42year old male who presented with fever and rapidly progressive respiratory symptoms like breathlessness, nonproductive cough and right sided chest pain. Initial imaging workup done at our hospital revealed a large unilateral tumor with tracheal shift. While being evaluated patient developed facial puffiness, tachypnea suggestive of superior vena cava obstruction. Antemortem biopsy of lung mass was attempted twice and that suggested malignant lesion. Unfortunately, the individual had a rapid downhill course following admission. Post mortem examination was conducted that on opening the thoracic cavity revealed total replacement of right lung tissue by a necrotic growth which was deeply adherent to the rib cage. The contralateral lung as well as all other visceral organs were unremarkable grossly. Histopathology confirmed primary Ewing sarcoma of the lung. We hereby, report a rare case of primary lung Ewing sarcoma diagnosed at autopsy.info:eu-repo/semantics/openAccessHospital Universitário da Universidade de São PauloAutopsy and Case Reports v.10 n.3 20202020-01-01info:eu-repo/semantics/reporttext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S2236-19602020000300401en10.4322/acr.2020.199
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country Brasil
countrycode BR
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databasecode rev-scielo-br
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region America del Sur
libraryname SciELO
language English
format Digital
author Gupta,Devika
Chatterjee,Tathagata
Tewari,Rohit
Trehan,Arti
Ahuja,Anuradha
spellingShingle Gupta,Devika
Chatterjee,Tathagata
Tewari,Rohit
Trehan,Arti
Ahuja,Anuradha
Primary Ewing sarcoma/primitive neuroectodermal tumor of the lung
author_facet Gupta,Devika
Chatterjee,Tathagata
Tewari,Rohit
Trehan,Arti
Ahuja,Anuradha
author_sort Gupta,Devika
title Primary Ewing sarcoma/primitive neuroectodermal tumor of the lung
title_short Primary Ewing sarcoma/primitive neuroectodermal tumor of the lung
title_full Primary Ewing sarcoma/primitive neuroectodermal tumor of the lung
title_fullStr Primary Ewing sarcoma/primitive neuroectodermal tumor of the lung
title_full_unstemmed Primary Ewing sarcoma/primitive neuroectodermal tumor of the lung
title_sort primary ewing sarcoma/primitive neuroectodermal tumor of the lung
description ABSTRACT We present the autopsy findings and differential diagnosis in a 42year old male who presented with fever and rapidly progressive respiratory symptoms like breathlessness, nonproductive cough and right sided chest pain. Initial imaging workup done at our hospital revealed a large unilateral tumor with tracheal shift. While being evaluated patient developed facial puffiness, tachypnea suggestive of superior vena cava obstruction. Antemortem biopsy of lung mass was attempted twice and that suggested malignant lesion. Unfortunately, the individual had a rapid downhill course following admission. Post mortem examination was conducted that on opening the thoracic cavity revealed total replacement of right lung tissue by a necrotic growth which was deeply adherent to the rib cage. The contralateral lung as well as all other visceral organs were unremarkable grossly. Histopathology confirmed primary Ewing sarcoma of the lung. We hereby, report a rare case of primary lung Ewing sarcoma diagnosed at autopsy.
publisher Hospital Universitário da Universidade de São Paulo
publishDate 2020
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S2236-19602020000300401
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AT trehanarti primaryewingsarcomaprimitiveneuroectodermaltumorofthelung
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