Proximal-type epithelioid sarcoma - Case report

Proximal-type epithelioid sarcoma - Case report

Epithelioid sarcoma, first described by Enzinger in 1970, is a rare soft-tissue sarcoma typically presenting as a subcutaneous or deep dermal mass in distal portions of the extremities of adolescents and young adults. In 1997, Guillou et al. described a different type of epithelioid sarcoma, called proximal-type epithelioid sarcoma, which is found mostly in the pelvic and perineal regions and genital tracts of young to middle-aged adults. It is characterized by a proliferation of epithelioid-like cells with rhabdoid features and the absence of a granuloma-like pattern. In this paper we present a case of proximal-type epithelioid sarcoma with an aggressive clinical course, including distant metastasis and death nine months after diagnosis.

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Main Authors: Santos,Luciana Mendes dos, Nogueira,Lisiane, Matsuo,Christiane Yuri, Talhari,Carolina, Santos,Monica
Format: Digital revista
Language:English
Published: Sociedade Brasileira de Dermatologia 2013
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000300444
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spelling oai:scielo:S0365-059620130003004442013-06-26Proximal-type epithelioid sarcoma - Case reportSantos,Luciana Mendes dosNogueira,LisianeMatsuo,Christiane YuriTalhari,CarolinaSantos,Monica Diagnosis Diagnosis, differential Sarcoma Therapeutics Epithelioid sarcoma, first described by Enzinger in 1970, is a rare soft-tissue sarcoma typically presenting as a subcutaneous or deep dermal mass in distal portions of the extremities of adolescents and young adults. In 1997, Guillou et al. described a different type of epithelioid sarcoma, called proximal-type epithelioid sarcoma, which is found mostly in the pelvic and perineal regions and genital tracts of young to middle-aged adults. It is characterized by a proliferation of epithelioid-like cells with rhabdoid features and the absence of a granuloma-like pattern. In this paper we present a case of proximal-type epithelioid sarcoma with an aggressive clinical course, including distant metastasis and death nine months after diagnosis.info:eu-repo/semantics/openAccessSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia v.88 n.3 20132013-06-01info:eu-repo/semantics/reporttext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000300444en10.1590/abd1806-4841.20131922
institution SCIELO
collection OJS
country Brasil
countrycode BR
component Revista
access En linea
databasecode rev-scielo-br
tag revista
region America del Sur
libraryname SciELO
language English
format Digital
author Santos,Luciana Mendes dos
Nogueira,Lisiane
Matsuo,Christiane Yuri
Talhari,Carolina
Santos,Monica
spellingShingle Santos,Luciana Mendes dos
Nogueira,Lisiane
Matsuo,Christiane Yuri
Talhari,Carolina
Santos,Monica
Proximal-type epithelioid sarcoma - Case report
author_facet Santos,Luciana Mendes dos
Nogueira,Lisiane
Matsuo,Christiane Yuri
Talhari,Carolina
Santos,Monica
author_sort Santos,Luciana Mendes dos
title Proximal-type epithelioid sarcoma - Case report
title_short Proximal-type epithelioid sarcoma - Case report
title_full Proximal-type epithelioid sarcoma - Case report
title_fullStr Proximal-type epithelioid sarcoma - Case report
title_full_unstemmed Proximal-type epithelioid sarcoma - Case report
title_sort proximal-type epithelioid sarcoma - case report
description Epithelioid sarcoma, first described by Enzinger in 1970, is a rare soft-tissue sarcoma typically presenting as a subcutaneous or deep dermal mass in distal portions of the extremities of adolescents and young adults. In 1997, Guillou et al. described a different type of epithelioid sarcoma, called proximal-type epithelioid sarcoma, which is found mostly in the pelvic and perineal regions and genital tracts of young to middle-aged adults. It is characterized by a proliferation of epithelioid-like cells with rhabdoid features and the absence of a granuloma-like pattern. In this paper we present a case of proximal-type epithelioid sarcoma with an aggressive clinical course, including distant metastasis and death nine months after diagnosis.
publisher Sociedade Brasileira de Dermatologia
publishDate 2013
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000300444
work_keys_str_mv AT santoslucianamendesdos proximaltypeepithelioidsarcomacasereport
AT nogueiralisiane proximaltypeepithelioidsarcomacasereport
AT matsuochristianeyuri proximaltypeepithelioidsarcomacasereport
AT talharicarolina proximaltypeepithelioidsarcomacasereport
AT santosmonica proximaltypeepithelioidsarcomacasereport
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