Colangiocarcinoma primario asociado a enfermedad de Caroli

A 68 years old male presented with right hypochondrium abdominal pain and jaundice with no other clinical finding. CAT Scan and Ultrasonography showed right lobe bile duct dilatation. Magnetic Resonance Cholangiopancreatography gave an outstanding vision of a restricted right lobe bile duct dilatation associated to choledocholithiasis. A right hepatectomy and bile duct exploration were performed. The histopathological study disclosed a Caroli disease associated to a primary cholangiocarcinoma. Caroli disease is a congenital disorder characterized by intrahepatic cystic bile duct dilatation with a high risk association with cholangiocarcinoma (Rev Méd Chile 2001; 129: 1433-8)

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Main Authors: Faría O,Gaspar, de Aretxabala U,Xabier, Sierralta Z,Armando, Flores O,Plácido, Burgos SJ,Luis
Format: Digital revista
Language:Spanish / Castilian
Published: Sociedad Médica de Santiago 2001
Online Access:http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872001001200009
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spelling oai:scielo:S0034-988720010012000092005-11-22Colangiocarcinoma primario asociado a enfermedad de CaroliFaría O,Gasparde Aretxabala U,XabierSierralta Z,ArmandoFlores O,PlácidoBurgos SJ,Luis Caroli disease Cholangiocarcinoma Cholangio-pancreatography Magnetic resonance imaging A 68 years old male presented with right hypochondrium abdominal pain and jaundice with no other clinical finding. CAT Scan and Ultrasonography showed right lobe bile duct dilatation. Magnetic Resonance Cholangiopancreatography gave an outstanding vision of a restricted right lobe bile duct dilatation associated to choledocholithiasis. A right hepatectomy and bile duct exploration were performed. The histopathological study disclosed a Caroli disease associated to a primary cholangiocarcinoma. Caroli disease is a congenital disorder characterized by intrahepatic cystic bile duct dilatation with a high risk association with cholangiocarcinoma (Rev Méd Chile 2001; 129: 1433-8)info:eu-repo/semantics/openAccessSociedad Médica de SantiagoRevista médica de Chile v.129 n.12 20012001-12-01text/htmlhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872001001200009es10.4067/S0034-98872001001200009
institution SCIELO
collection OJS
country Chile
countrycode CL
component Revista
access En linea
databasecode rev-scielo-cl
tag revista
region America del Sur
libraryname SciELO
language Spanish / Castilian
format Digital
author Faría O,Gaspar
de Aretxabala U,Xabier
Sierralta Z,Armando
Flores O,Plácido
Burgos SJ,Luis
spellingShingle Faría O,Gaspar
de Aretxabala U,Xabier
Sierralta Z,Armando
Flores O,Plácido
Burgos SJ,Luis
Colangiocarcinoma primario asociado a enfermedad de Caroli
author_facet Faría O,Gaspar
de Aretxabala U,Xabier
Sierralta Z,Armando
Flores O,Plácido
Burgos SJ,Luis
author_sort Faría O,Gaspar
title Colangiocarcinoma primario asociado a enfermedad de Caroli
title_short Colangiocarcinoma primario asociado a enfermedad de Caroli
title_full Colangiocarcinoma primario asociado a enfermedad de Caroli
title_fullStr Colangiocarcinoma primario asociado a enfermedad de Caroli
title_full_unstemmed Colangiocarcinoma primario asociado a enfermedad de Caroli
title_sort colangiocarcinoma primario asociado a enfermedad de caroli
description A 68 years old male presented with right hypochondrium abdominal pain and jaundice with no other clinical finding. CAT Scan and Ultrasonography showed right lobe bile duct dilatation. Magnetic Resonance Cholangiopancreatography gave an outstanding vision of a restricted right lobe bile duct dilatation associated to choledocholithiasis. A right hepatectomy and bile duct exploration were performed. The histopathological study disclosed a Caroli disease associated to a primary cholangiocarcinoma. Caroli disease is a congenital disorder characterized by intrahepatic cystic bile duct dilatation with a high risk association with cholangiocarcinoma (Rev Méd Chile 2001; 129: 1433-8)
publisher Sociedad Médica de Santiago
publishDate 2001
url http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872001001200009
work_keys_str_mv AT fariaogaspar colangiocarcinomaprimarioasociadoaenfermedaddecaroli
AT dearetxabalauxabier colangiocarcinomaprimarioasociadoaenfermedaddecaroli
AT sierraltazarmando colangiocarcinomaprimarioasociadoaenfermedaddecaroli
AT floresoplacido colangiocarcinomaprimarioasociadoaenfermedaddecaroli
AT burgossjluis colangiocarcinomaprimarioasociadoaenfermedaddecaroli
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